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Truncus arteriosus with interrupted aortic arch
Truncus arteriosus with interrupted aortic arch





truncus arteriosus with interrupted aortic arch

Freedom from reintervention for arch obstruction was 60% at 5 years. Truncus arteriosus (TA) is a conotruncal anomaly in which a single great vessel arises from the heart and. Truncus arteriosus The primitive truncus does not divide into the pulmonary artery and aorta, resulting in a single large arterial trunk that overlies a large ventricular septal defect. Greatest survival occurred in those patients with uncomplicated IAA who had repair since 1993 (5 year survival, 83%). A severe form of truncus arteriosus is one associated with an interrupted aortic arch. Early and constant-hazard phases were noted, with incremental risk factors for early phase mortality being cyanosis at presentation, presence of truncus arteriosus or aortic stenosis, an episode of circulatory collapse before repair, earlier date of repair, and lower weight at repair. Overall survival after repair was 50% at age 1 month, 35% at 1 year, and 34% at 5 years. Independent risk factors for death without IAA repair (p < 0.001) included absence of ventricular septal defect, and the presence of noncardiac anomaly, complex cardiac anomaly, episode of acidosis and earlier birth cohort. The median age was 6.5 days (range 1-85 days) and median weight was 3.2 kg (range 2.6-4.8 kg). Methods: Between 19, eight consecutive patients underwent repair of truncus arteriosus with interrupted aortic arch. Significant trends over time for patients born in three consecutive periods (1975 to 1984, 1985 to 1993, and 1994 to 1999) demonstrated a smaller proportion of patients with presentation with circulatory collapse (65%, 51%, and 25%, respectively), greater use of prostaglandins (72%, 90%, 100%), fewer deaths without IAA repair (49%, 15%, 13%) and greater use of one-stage repair (68%, 75%, 100%). Objective: The aim of our study was to analyse experience with repair of truncus arteriosus with interrupted aortic arch. On postnatal day 30 (1378 g), we performed bilateral. We reviewed all consecutive patients (n = 119) presenting from 1975 to 1999, and data were collected regarding demographics, anatomy, management and outcomes. A neonate, born after 29 weeks and 2 days gestation (weight 1015 g), was diagnosed with truncus arteriosus and interrupted aortic arch. (Ao aorta LSA left subclavian artery. We report long-term follow-up after one-stage repair of TA associated with IAA. We sought to determine trends in presentation, management, outcomes and associated factors. Anatomy of the aortic arch interruption and truncus arteriosus in 50 neonates. Background: Truncus arteriosus (TA) with interrupted aortic arch (IAA) is a rare combination of complex anomalies. Interrupted aortic arch (IAA) continues to be associated with important mortality, both before and immediately after repair, with ongoing morbidity during follow-up.







Truncus arteriosus with interrupted aortic arch